Disease presentation

The disease is characterized by recurrent symptoms of acute pericardiatis with symptoms reappearing after a disease-free period of 4-6 weeks.

Main clinical symptoms

Chest pain

Heart membrane (pericardium) inflammation as highlighted by imaging techniques

Fever

Biological signs

Increase of erythrocyte sedimentation rate

Increase of C-reactive protein (CRP)

Increase of white blood cell count

Therapy

• Non-steroidal anti-inflammatory drugs/aspirin combined with Colchicine
• Corticosteroids
• Anti-IL-1 (Anakinra)
• Immunosuppressive drugs (azathioprine)