BEHCET

web Behcet
Epidemiology

Turquoise gender

Gender ratio

1:1

Turquoise age

Average onset age

15-45y

Turquoise incidence

Incidence

1-420/105

Disease presentation

The disease is characterized by the chronic inflammation of blood vessels. The International Criteria for Behçet's Disease (ICBD) have been established to facilitate the diagnosis.

Main clinical symptoms

picto feverFever

picto Muco cutanneousMouth and genital ulcers

picto skin rashSkin rash

picto UveltisUveitis (red eye)

picto vessel inflamVessel inflammation

NB: Other possible involvement: joint, neurologic, digestive, vasculatory

Biological signs

Turquoise upIncrease in C-reactive protein (CRP)

Turquoise presentPresence of HLA-B51

Therapy

  • Colchicine
  • Non-steroidal anti-inflammatory drugs
  • Corticosteroids
  • Immunomodulating drugs